表1. ACR/EULAR 系统性硬化症分类标准

主要条目                                                                      亚条目                                       权重/评分复旦大学附属华东医院免疫风湿科申艳

双手指皮肤增厚并渐近至掌指关节（足以诊断）     -                                                     9

手指皮肤增厚（仅计最高评分）                           手指肿胀                                             2

                                                                                  指端硬化（不及MCP但渐近PIP）    4

指端损害（仅计最高评分）                                   指尖溃疡                                              2

                                                                                    指尖凹陷性疤痕                                 3

毛细血管扩张                                                                         -                                               2

甲襞毛细血管异常                                                                 -                                               2

肺动脉高压和/或间质性肺病（最高2分）               肺动脉高压                                       2

                                                                                      间质性肺病                                        2

雷诺现象                                                                              -                                                  3

SSc相关抗体（最高3分）                                     抗着丝点抗体                                       3

                                                                                  抗拓扑异构酶I抗体（抗Scl-70）

                                                                                    抗RNA聚合酶III抗体

注：总得分为各项最高评分的总和。总得分>9分即可归类为SSc患者